Human CFTR (Cystic Fibrosis Transmembrane Conductance Regulator) ELISA Kit
Contáctenos para saber el precio
Por favor contáctenos para obtener información detallada sobre el precio y disponibilidad.
Name
Human CFTR (Cystic Fibrosis Transmembrane Conductance Regulator) ELISA Kit
Category
ELISA Kits
Provider
FineTest
Reference
EH2805
Tested Applications
ELISA
Documentos del producto
Instrucciones
Data sheet
Especificaciones del producto
| Category | ELISA Kits |
| Reactivity | Human |
| Detection Method | Colorimetric |
| Assay Data | 4 hours |
| Assay Type | Sandwich ELISA, Double Antibody |
| Test Range | 0.156-10ng/ml |
| Sensitivity | 0.094ng/ml |
| Size 1 | 96T |
| Tested Applications | ELISA |
| Sample Type | Serum, Plasma, Cell Culture Supernatant, cell or tissue lysate, Other liquid samples |
| Availability | Shipped within 10-14 working days. |
| Storage | 2-8 °C for 12 months |
| UniProt ID | P13569 |
| Alias | ATP-binding cassette sub-family C member 7,CF,MRP7,ABC35,ABCC7,CFTR/MRP,TNR-CFTR,dJ760C5.1,Cystic fibrosis transmembrane conductance regulator,Channel conductance-controlling ATPase |
| Background | Elisa kits for CFTR |
| Status | RUO |
Background
CF Transmembrane Conductance Regulator (ABCC7), widely known as the cystic fibrosis transmembrane conductance regulator (CFTR), is a chloride channel essential for maintaining ion and water balance across epithelial cell membranes. Mutations in the CFTR gene cause cystic fibrosis (CF), a life-threatening genetic disorder that leads to thick mucus buildup in the lungs, pancreas, and other organs. As an ATP-gated channel, ABCC7 regulates chloride and bicarbonate secretion, influencing fluid viscosity and pH in various tissues. Beyond ion transport, CFTR modulates inflammation and immune responses, contributing to its broader physiological significance. Therapeutic interventions targeting CFTR, such as small-molecule modulators, have revolutionized CF management, improving lung function and quality of life for many patients. Additionally, CFTR dysfunction has been implicated in other conditions like chronic obstructive pulmonary disease (COPD) and pancreatitis, underlining its relevance in diverse respiratory and gastrointestinal diseases.
Productos relacionados
Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Antibody
CFTR Antibody is a Rabbit Polyclonal Antibody against CFTR.…
Ver producto
Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Antibody
Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Antibody is a Rabbit Polyclonal antibody for the detection of…
Ver producto
Human Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) ELISA Kit
Human Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) ELISA Kit is an ELISA Kit for the in vitro quantitative…
Ver producto