Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Antibody

Este producto es parte de ABCC - ATP binding cassette subfamily C
Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Antibody
286€ (100 µl)

Por favor contáctenos para obtener información detallada sobre el precio y disponibilidad.

Name
Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Antibody
Category
Primary Antibodies
Provider
Abbexa
Reference
abx176077
Tested Applications
IHC

Description

Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Antibody is a Rabbit Polyclonal antibody against Cystic Fibrosis Transmembrane Conductance Regulator (CFTR).

Documentos del producto

Instrucciones
Data sheet
Descargar

Especificaciones del producto

Category
Primary Antibodies
Immunogen Target
Target: Cystic Fibrosis Transmembrane Conductance Regulator (CFTR)
Immunogen: CFTR (Gln359-Ser858)
Host
Rabbit
Reactivity
Human
Recommended Dilution
WB (Predicted): 0.01-2 µg/ml, IHC: 5-20 µg/ml, IF/ICC (Predicted): 5-20 µg/ml. Optimal dilutions/concentrations should be determined by the end user.
Clonality
Polyclonal
Conjugation
Unconjugated
Purification
Purified by antigen-specific affinity chromatography, followed by Protein A affinity chromatography.
Size 1
100 µl
Size 2
200 µl
Size 3
1 ml
Form
Liquid
Tested Applications
IHC
Buffer
0.01 M PBS, pH 7.4, containing 0.05% Proclin-300, 50% glycerol.
Availability
Shipped within 5-7 working days.
Storage
Aliquot and store at -20°C. Avoid repeated freeze/thaw cycles.
Dry Ice
No
Alias
ATP-binding cassette sub-family C member 7,CF,MRP7,ABC35,ABCC7,CFTR/MRP,TNR-CFTR,dJ760C5.1,Cystic fibrosis transmembrane conductance regulator,Channel conductance-controlling ATPase
Background
Antibody anti-CFTR
Status
RUO
Note
THIS PRODUCT IS FOR RESEARCH USE ONLY. NOT FOR USE IN DIAGNOSTIC, THERAPEUTIC OR COSMETIC PROCEDURES. NOT FOR HUMAN OR ANIMAL CONSUMPTION.

Background

CF Transmembrane Conductance Regulator (ABCC7), widely known as the cystic fibrosis transmembrane conductance regulator (CFTR), is a chloride channel essential for maintaining ion and water balance across epithelial cell membranes. Mutations in the CFTR gene cause cystic fibrosis (CF), a life-threatening genetic disorder that leads to thick mucus buildup in the lungs, pancreas, and other organs. As an ATP-gated channel, ABCC7 regulates chloride and bicarbonate secretion, influencing fluid viscosity and pH in various tissues. Beyond ion transport, CFTR modulates inflammation and immune responses, contributing to its broader physiological significance. Therapeutic interventions targeting CFTR, such as small-molecule modulators, have revolutionized CF management, improving lung function and quality of life for many patients. Additionally, CFTR dysfunction has been implicated in other conditions like chronic obstructive pulmonary disease (COPD) and pancreatitis, underlining its relevance in diverse respiratory and gastrointestinal diseases.

Productos relacionados

abx005919

Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Antibody

CFTR Antibody is a Rabbit Polyclonal Antibody against CFTR.…

Ver producto
abx149257

Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Antibody

Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Antibody is a Rabbit Polyclonal antibody for the detection of…

Ver producto
abx151043

Human Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) ELISA Kit

Human Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) ELISA Kit is an ELISA Kit for the in vitro quantitative…

Ver producto