Porphobilinogen deaminase (HMBS) Antibody

Por favor contáctenos para obtener información detallada sobre el precio y disponibilidad.
Description
Porphobilinogen deaminase (HMBS) Antibody is a Recombinant Rabbit Monoclonal antibody for the detection of Human HMBS.
Documents del producto
Product specifications
Category | Primary Antibodies |
Immunogen Target | Porphobilinogen deaminase (HMBS) |
Host | Rabbit |
Reactivity | Human |
Recommended Dilution | WB: 1/500 - 1/2000. Optimal dilutions/concentrations should be determined by the end user. |
Clonality | Monoclonal |
Conjugation | Unconjugated |
Isotype | IgG |
Expression | Recombinant |
Purification | Purified by affinity chromatography. |
Size 1 | 50 µl |
Size 2 | 100 µl |
Form | Liquid |
Tested Applications | ELISA, WB |
Buffer | PBS, pH 7.4, 150 mM NaCl, 0.02% sodium azide and 50% glycerol. |
Availability | Shipped within 5-10 working days. |
Storage | Aliquot and store at -20°C. Avoid repeated freeze/thaw cycles. |
Dry Ice | No |
UniProt ID | P08397 |
Gene ID | 3145 |
OMIM | 176000 |
Background | Antibody anti-HMBS |
Status | RUO |
Descripción
Related Products

HMBS antibody
Tetrapolymerization of the monopyrrole PBG into the hydroxymethylbilane pre-uroporphyrinogen in several discrete steps.
Ver Producto
Recombinant Human HMBS
Ver Producto
Porphobilinogen Deaminase (HMBS) Antibody
HMBS Antibody is a Rabbit Polyclonal antibody against HMBS. This gene encodes a member of the hydroxymethylbilane synthase superfamily. The encoded protein is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in this gene are associated with the autosomal dominant disease acute intermittent porphyria. Alternatively spliced transcript variants encoding different isoforms have been described. [provided by RefSeq, Jul 2008].
Ver Producto