HMBS antibody
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Description
Tetrapolymerization of the monopyrrole PBG into the hydroxymethylbilane pre-uroporphyrinogen in several discrete steps.
Documents del producto
Product specifications
| Category | Primary Antibodies |
| Immunogen Target | hydroxymethylbilane synthase (HMBS) |
| Host | Rabbit |
| Reactivity | Human, Mouse, Rat |
| Recommended Dilution | WB: 1:500-1:2000; IF: 1:20-1:200 |
| Clonality | polyclonal |
| Conjugation | Unconjugated |
| Isotype | IgG |
| Observed MW | 39-42kd |
| Purity | ≥95% as determined by SDS-PAGE |
| Purification | Immunogen affinity purified |
| Size 1 | 100µg |
| Form | liquid |
| Tested Applications | ELISA, WB, IF |
| Storage | PBS with 0.02% sodium azide and 50% glycerol pH 7.3, -20℃ for 12 months(Avoid repeated freeze / thaw cycles.) |
| UniProt ID | P08397 |
| Gene ID | 3145 |
| Alias | Porphobilinogen deaminase (PBG-D),Hydroxymethylbilane synthase (HMBS),Pre-uroporphyrinogen synthase,HMBS,PBGD,UPS |
| Background | Antibody anti-HMBS |
| Status | RUO |
| Note | Mol. Weight 39-42 kDa |
Descripción
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HMBS antibody
Tetrapolymerization of the monopyrrole PBG into the hydroxymethylbilane pre-uroporphyrinogen in several discrete steps.
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HMBS Antibody is a Rabbit Polyclonal antibody against HMBS. This gene encodes a member of the hydroxymethylbilane synthase superfamily. The encoded protein is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in this gene are associated with the autosomal dominant disease acute intermittent porphyria. Alternatively spliced transcript variants encoding different isoforms have been described. [provided by RefSeq, Jul 2008].
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