N-Acetylgalactosamine 6-Sulfatase (GALNS) Antibody
195€ (20 µl)
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935106861
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name
N-Acetylgalactosamine 6-Sulfatase (GALNS) Antibody
category
Primary Antibodies
provider
Abbexa
reference
abx004181
tested applications
ELISA, WB, IF/ICC
Description
GALNS Antibody is a Rabbit Polyclonal antibody against GALNS. This gene encodes N-acetylgalactosamine-6-sulfatase which is a lysosomal exohydrolase required for the degradation of the glycosaminoglycans, keratan sulfate, and chondroitin 6-sulfate. Sequence alterations including point, missense and nonsense mutations, as well as those that affect splicing, result in a deficiency of this enzyme. Deficiencies of this enzyme lead to Morquio A syndrome, a lysosomal storage disorder.
Documents del producto
Instrucciones
Data sheet
Product specifications
| Category | Primary Antibodies |
| Immunogen Target | N-Acetylgalactosamine 6-Sulfatase (GALNS) |
| Host | Rabbit |
| Reactivity | Human, Mouse, Rat |
| Recommended Dilution | ELISA: 1 µg/ml, WB: 1/500 - 1/2000, IF/ICC: 1/50 - 1/200. Optimal dilutions/concentrations should be determined by the end user. |
| Clonality | Polyclonal |
| Conjugation | Unconjugated |
| Isotype | IgG |
| Purification | Purified by affinity chromatography. |
| Size 1 | 20 µl |
| Size 2 | 100 µl |
| Size 3 | 2 × 100 µl |
| Form | Liquid |
| Tested Applications | ELISA, WB, IF/ICC |
| Buffer | PBS, pH 7.3, containing 0.02% sodium azide, 50% glycerol. |
| Availability | Shipped within 5-10 working days. |
| Storage | Aliquot and store at -20°C. Avoid repeated freeze/thaw cycles. |
| Dry Ice | No |
| UniProt ID | P34059 |
| Gene ID | 2588 |
| NCBI Accession | NP_000503.1 |
| OMIM | 253000 |
| Background | Antibody anti-GALNS |
| Status | RUO |
| Note | Concentration: 2.32 mg/ml - |
Descripción
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N-Acetylgalactosamine 6-Sulfatase (GALNS) Antibody
GALNS Antibody is a Rabbit Polyclonal antibody against GALNS. This gene encodes N-acetylgalactosamine-6-sulfatase which is a lysosomal exohydrolase required for the degradation of the glycosaminoglycans, keratan sulfate, and chondroitin 6-sulfate. Sequence alterations including point, missense and nonsense mutations, as well as those that affect splicing, result in a deficiency of this enzyme. Deficiencies of this enzyme lead to Morquio A syndrome, a lysosomal storage disorder.
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