Methylmalonate-Semialdehyde Dehydrogenase [acylating], Mitochondrial (ALDH6A1) Antibody

Descripción

This protein belongs to the aldehyde dehydrogenases family of proteins. This enzyme plays a role in the valine and pyrimidine catabolic pathways. The product of this gene, a mitochondrial methylmalonate semialdehyde dehydrogenase, catalyzes the irreversible oxidative decarboxylation of malonate and methylmalonate semialdehydes to acetyl and propionyl-CoA. Methylmalonate semialdehyde dehydrogenase deficiency is characterized by elevated beta-alanine, 3-hydroxypropionic acid, and both isomers of 3-amino and 3-hydroxyisobutyric acids in urine organic acids.

Características del producto

clonality

Monoclonal

reactivity

Human

immunogen target

Methylmalonate-Semialdehyde Dehydrogenase [acylating], Mitochondrial (ALDH6A1)

host

Mouse

conjugation

Unconjugated

form

Liquid

tested applications

ELISA, WB, IHC, IF/ICC

purification

Purified through a protein G column, eluted with high and low pH buffers and neutralized immediately, followed by dialysis against PBS.

buffer

PBS containing 0.09% sodium azide.

size 1

80 µl

size 2

400 µl

storage

Aliquot and store at -20°C. Avoid repeated freeze/thaw cycles.

or code

ALDH6A1

dry ice

availability

Shipped within 5-10 working days.

alias

ALDH6A1,MMSDH

uniprot id

https://www.uniprot.org/uniprotkb/Q02252

NCBI accession

NP_005580.1

note

This product is for research use only.

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anti- ALDH6A1 antibody

proveedor

FineTest

reference

FNab00298

Tested Applications

ELISA, WB, IHC

reactivity

human,mouse,rat

status

RUO

clonality

polyclonal

Plays a role in valine and pyrimidine metabolism. Binds fatty acyl-CoA.

Precio a consultar

Recombinant Human ALDH6A1