ATP Binding Cassette Subfamily D Member 2 (ABCD2) Antibody

Este producto es parte de ABCD - ATP Binding Cassette Transporter D
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416€ (200 µl)

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935106861
info@markelab.com
name
ATP Binding Cassette Subfamily D Member 2 (ABCD2) Antibody
category
Primary Antibodies
provider
Abbexa
reference
abx432266
tested applications
P-ELISA, WB

Description

ABCD2 Antibody is a Goat Polyclonal antibody against ABCD2.

Documents del producto

Instrucciones
Data sheet
Descargar

Product specifications

Category
Primary Antibodies
Immunogen Target
ATP Binding Cassette Subfamily D Member 2 (ABCD2)
Host
Goat
Reactivity
Human
Recommended Dilution
P-ELISA: 1/32000. Optimal dilutions/concentrations should be determined by the end user.
Clonality
Polyclonal
Conjugation
Unconjugated
Isotype
IgG
Purification
Purified from goat serum by ammonium sulphate precipitation followed by antigen affinity chromatography using the immunizing peptide.
Size 1
200 µl
Form
Liquid
Tested Applications
P-ELISA, WB
Buffer
Tris saline, pH 7.3, containing 0.02% sodium azide and 0.5% bovine serum albumin.
Availability
Shipped within 5-10 working days.
Storage
Aliquot and store at -20°C. Avoid repeated freeze/thaw cycles.
Dry Ice
No
Gene ID
225
NCBI Accession
NP_005155.1
Alias
ABC39,ALDL1,ALDR,ALDRP
Background
Antibody anti-ABCD2
Status
RUO
Note
Concentration: 0.5 mg/ml - 

Descripción

ABCD2 is a peroxisomal ATP-binding cassette transporter that plays a key role in the import of very-long-chain fatty acids (VLCFAs) and their derivatives into peroxisomes for β-oxidation. It is highly expressed in tissues such as the liver, brain, and adrenal glands, where VLCFA metabolism is essential for cellular function and homeostasis. Structurally, ABCD2 contains nucleotide-binding domains that drive ATP-dependent substrate transport across the peroxisomal membrane. ABCD2 shares functional redundancy with ABCD1, compensating for its loss in certain conditions such as X-linked adrenoleukodystrophy (X-ALD). Dysregulation of ABCD2 expression has been associated with metabolic disorders involving lipid accumulation and peroxisomal dysfunction, highlighting its importance in lipid metabolism and cellular health.

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