BCKDHB antibody
Por favor contáctenos para obtener información detallada sobre el precio y disponibilidad.
Description
The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase(E1), lipoamide acyltransferase(E2) and lipoamide dehydrogenase(E3).
Documents del producto
Product specifications
| Category | Primary Antibodies |
| Immunogen Target | branched chain keto acid dehydrogenase E1, beta polypeptide (BCKDHB) |
| Host | Rabbit |
| Reactivity | Human, Mouse, Rat |
| Recommended Dilution | WB: 1:500-1:2000; IHC: 1:20-1:200 |
| Clonality | polyclonal |
| Conjugation | Unconjugated |
| Isotype | IgG |
| Observed MW | 43 kDa |
| Purity | ≥95% as determined by SDS-PAGE |
| Purification | Immunogen affinity purified |
| Size 1 | 100µg |
| Form | liquid |
| Tested Applications | ELISA, WB, IHC |
| Storage | PBS with 0.02% sodium azide and 50% glycerol pH 7.3, -20℃ for 12 months(Avoid repeated freeze / thaw cycles.) |
| UniProt ID | P21953 |
| Gene ID | 594 |
| Alias | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial,Branched-chain alpha-keto acid dehydrogenase E1 component beta chain (BCKDE1B, BCKDH E1-beta),BCKDHB |
| Background | Antibody anti-BCKDHB |
| Status | RUO |
| Note | Mol. Weight 43 kDa |
Descripción
Related Products
Human BCKDHB (2-Oxoisovalerate Dehydrogenase Subunit Beta, Mitochondrial) ELISA Kit
Ver Producto
BCKDHB antibody
The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase(E1), lipoamide acyltransferase(E2) and lipoamide dehydrogenase(E3).
Ver Producto
2-Oxoisovalerate Dehydrogenase Subunit Beta, Mitochondrial (BCKDHB) Antibody
Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems.
Ver Producto