Trifunctional Enzyme Subunit Alpha, Mitochondrial (HADHA) Antibody

260€ (50 µg)
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935106861
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name
Trifunctional Enzyme Subunit Alpha, Mitochondrial (HADHA) Antibody
category
Primary Antibodies
provider
Abbexa
reference
abx455317
tested applications
ELISA, WB, IHC
Description
Trifunctional Enzyme Subunit Alpha, Mitochondrial (HADHA) Antibody is a Rabbit polyclonal antibody for the detection of Human Trifunctional Enzyme Subunit Alpha, Mitochondrial (HADHA).
Documents del producto
Instrucciones
Data sheet
Product specifications
Category | Primary Antibodies |
Immunogen Target | Trifunctional Enzyme Subunit Alpha, Mitochondrial (HADHA) |
Host | Rabbit |
Reactivity | Human |
Recommended Dilution | Optimal dilutions/concentrations should be determined by the end user. |
Clonality | Polyclonal |
Conjugation | Unconjugated |
Isotype | IgG |
Size 1 | 50 µg |
Size 2 | 100 µg |
Form | Liquid |
Tested Applications | ELISA, WB, IHC |
Buffer | 0.01 M PBS, pH 7.4, 50% glycerol, 0.05% Proclin-300. |
Availability | Shipped within 5-12 working days. |
Storage | Store at 2-8 °C for up to 2 weeks. For long-term storage, aliquot and store at -80 °C. Avoid repeated freeze/thaw cycles. |
Dry Ice | No |
UniProt ID | P40939 |
Gene ID | 3030 |
NCBI Accession | NP_000173.2 |
Background | Antibody anti-HADHA |
Status | RUO |
Descripción
Related Products

HADHA antibody
This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.
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