Human Very Long-Chain Specific Acyl-CoA Dehydrogenase, Mitochondrial (ACADVL) ELISA Kit
715€ (96 tests)
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935106861
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name
Human Very Long-Chain Specific Acyl-CoA Dehydrogenase, Mitochondrial (ACADVL) ELISA Kit
category
ELISA Kits
provider
Abbexa
reference
abx385572
tested applications
ELISA
Description
Human Very Long-Chain Specific Acyl-CoA Dehydrogenase, Mitochondrial (ACADVL) ELISA Kit is an ELISA Kit for the in vitro quantitative measurement of Human Very Long-Chain Specific Acyl-CoA Dehydrogenase, Mitochondrial (ACADVL) concentrations in tissue homogenates, cell lysates and other biological fluids.
Documents del producto
Product specifications
| Category | ELISA Kits |
| Immunogen Target | Very Long-Chain Specific Acyl-CoA Dehydrogenase, Mitochondrial (ACADVL) |
| Reactivity | Human |
| Detection Method | Colorimetric |
| Assay Data | Quantitative |
| Assay Type | Sandwich |
| Test Range | 0.156 ng/ml - 10 ng/ml |
| Sensitivity | < 0.06 ng/ml |
| Recommended Dilution | Optimal dilutions/concentrations should be determined by the end user. |
| Size 1 | 96 tests |
| Size 2 | 5 × 96 tests |
| Size 3 | 10 × 96 tests |
| Form | Lyophilized |
| Tested Applications | ELISA |
| Sample Type | Tissue homogenates, cell lysates and other biological fluids. |
| Availability | Shipped within 5-12 working days. The validity for this kit is at least 6 months. Up to 12 months validity can be provided on request. |
| Storage | Shipped at 4 °C. Upon receipt, store the kit according to the storage instruction in the kit's manual. |
| Dry Ice | No |
| UniProt ID | P49748 |
| Gene ID | 37 |
| OMIM | 201475 |
| Alias | ACAD6,LCACD,VLCAD |
| Background | Elisa kits for ACADVL |
| Status | RUO |
| Note | Validity: The validity for this kit is at least 6 months. Up to 12 months validity can be provided on request. This product is for research use only. The range and sensitivity is subject to change. Please contact us for the latest product information. For accurate results, sample concentrations must be diluted to mid-range of the kit. If you require a specific range, please contact us in advance or write your request in your order comments. Please note that our ELISA and CLIA kits are optimised for detection of native samples, rather than recombinant proteins. We are unable to guarantee detection of recombinant proteins, as they may have different sequences or tertiary structures to the native protein. |
Descripción
The ACADVL gene encodes the enzyme acyl-CoA dehydrogenase very long chain, which plays a vital role in the initial step of the mitochondrial fatty acid beta-oxidation pathway. Specifically, it is targeted to the inner mitochondrial membrane and is specific to long-chain and very-long-chain fatty acids. Mutations in this gene are associated with very long-chain acyl-coenzyme A dehydrogenase deficiency, leading to reduced myocardial fatty acid beta-oxidation and cardiomyopathy. Alternative splicing generates multiple transcript variants encoding different isoforms of the enzyme
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