Human ATP Binding Cassette Transporter A3 (ABCA3) CLIA Kit

Este producto es parte de ABCA3 - ATP Binding Cassette Transporter A3
Human ATP Binding Cassette Transporter A3 (ABCA3) CLIA Kit

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935106861

info@markelab.com

Precio

812.5€ (96 tests)

CLIA Kits ABCA3

proveedor

Abbexa

reference

abx494332

Tested Applications

CLIA

reactivity

Human

status

RUO

clonality

Descripción

Human ATP Binding Cassette Transporter A3 (ABCA3) Chemiluminescent Immunoassay (CLIA) Kit is a Sandwich Chemiluminescent Immunoassay (CLIA) Kit for use with Tissue homogenates and other biological fluids.


Human ATP Binding Cassette Transporter A3 (ABCA3) CLIA Kit es un kit CLIA tipo Sandwich para su uso con homogeneizados de tejido y otros fluidos biológicos.


Background

ABCA3 is a critical protein in pulmonary surfactant production, predominantly expressed in alveolar type II epithelial cells in the lungs. It plays an essential role in transporting phospholipids and cholesterol into lamellar bodies, which are specialized organelles where surfactant is stored before secretion. ABCA3 utilizes ATP hydrolysis to facilitate lipid transport, ensuring the proper composition and function of surfactant, which reduces surface tension in the alveoli and prevents lung collapse. Mutations in the ABCA3 gene are associated with surfactant metabolism disorders, including neonatal respiratory distress syndrome and interstitial lung disease. These conditions are characterized by impaired surfactant production, leading to respiratory failure. ABCA3’s function in lipid transport and its critical role in pulmonary physiology underscore its importance in respiratory health.

Características del producto

category

CLIA Kits


immunogen target

ATP Binding Cassette Transporter A3 (ABCA3)


reactivity

Human


test range

78.12 pg/ml - 5000 pg/ml


sensitivity

< 33 pg/ml


assay type

Sandwich


assay data

Quantitative


detection method

Chemiluminescent


sample type

Tissue homogenates and other biological fluids.


size 1

96 tests


size 2

5 × 96 tests


size 3

10 × 96 tests


alias

ABC-C,ABC3,LBM180,SMDP3


storage

Enviado a 4 °C. Una vez recibido, almacene el kit de acuerdo con las instrucciones citadas en el manual del kit


or code

ABCA3


dry ice

No


note

El rango y la sensibilidad pueden variar. Le recomendamos contactar con nosotros a fin de obtener la última información sobre posibles actualizaciones, que no estén representadas en este catalogo. Si necesita un rango específico, contáctenos y trataremos de ayudarle. Consulte sobre posible información que pueda ayudarle a elegir la dilución apropiada para sus muestras. Los kits CLIA están optimizados para la detección de muestras nativas, las proteínas recombinantes, pueden resultar problemáticas a causa de diferencias en la secuencia o cambios en la estructura terciaria.


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